Lymphangioleiomyoma
A neoplasm with perivascular epithelioid cell differentiation, often associated with tuberous sclerosis. It is characterized by the presence of smooth muscle and epithelioid cells and by the proliferation of lymphatic vessels. Sites of involvement include the lymph nodes, lung, mediastinum, and retroperitoneum.
Exact Synonyms
Lymphangioleiomyoma
Lymphangiomyoma
class Information
code
C3204
Contributing_Source
GDC
ICD-O-3_Code
9174/0
in_subset
Is_Value_For_GDC_Property
Legacy Concept Name
Lymphangiomyoma
Maps_To
- 9174/0
- Lymphangiomyoma
Neoplastic_Status
Undetermined
Preferred_Name
Lymphangioleiomyoma
Semantic_Type
Neoplastic Process
UMLS_CUI
C0024223