OntologiesncitclassesNCIT:C3794   
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Sex Cord-Stromal Tumor
http://purl.obolibrary.org/obo/NCIT_C3794

A neoplasm arising in the ovary or testis. It is composed of granulosa cells, Leydig cells, Sertoli cells, and fibroblasts. Each of these cell types may constitute the only cellular component that is present in the neoplasm or it may be mixed with other cell types in various combinations. The prognosis can not always be predicted on histologic grounds alone. Approximately, 10% of these tumors may metastasize. Representative examples include granulosa cell tumor, Leydig cell tumor, Sertoli cell tumor, and tumors of the thecoma-fibroma group.

Exact Synonyms
Gonadal stromal tumor, NOS
sex cord tumor
sex cord-gonadal stromal tumor
Sex Cord-Stromal Neoplasm
Sex Cord-Stromal Tumor
sex cord-stromal tumor
class Information
ALT_DEFINITION
  • A rare type of cancer that forms in the tissues that support the ovaries or testes. These tumors may release sex hormones. Sex cord-gonadal stromal tumors include granulosa cell, Sertoli cell, and Leydig cell tumors.
  • A tumor arising in the ovary or testis. It is composed of one or more of the following: granulosa cells, Leydig cells, Sertoli cells, and/or fibroblasts.
code

C3794

Contributing_Source
  • GDC
  • NICHD
ICD-O-3_Code

8590/1

Legacy Concept Name

Sex_Cord-Stromal_Tumor

Maps_To
  • 8590/1
  • Gonadal stromal tumor, NOS
  • Sex cord tumor, NOS
  • Sex cord-gonadal stromal tumor, NOS
Neoplastic_Status

Undetermined

Preferred_Name

Sex Cord-Stromal Tumor

Semantic_Type

Neoplastic Process

UMLS_CUI

C0206724

class Relations