Hydroa Vacciniforme Lymphoproliferative Disorder
A rare, EBV-positive cutaneous T-cell lymphoproliferative disorder, composed of CD8 positive cytotoxic T-lymphocytes. It affects children, almost exclusively in Latin America and Asia. Patients present with papulovesicular skin lesions, clinically resembling hydroa vacciniforme, in areas of sun-exposed skin.
Exact Synonyms
HV LPD
HV-Like LPD
HV-Like Lymphoma
HV-LPD
Hydroa Vacciniforme Lymphoproliferative Disorder
Hydroa Vacciniforme-Like Cutaneous T-Cell Lymphoma
Hydroa vacciniforme-like lymphoma
Hydroa Vacciniforme-Like Lymphoma
Hydroa Vacciniforme-Like Lymphoproliferative Disorder
class Information
ALT_DEFINITION
In contrast to hydroa vacciniforme (HV), HV-like lymphoma is not induced by sun exposure and the lesions can occur in both sun-exposed and covered body areas. It affects children, almost exclusively in Latin America and Asia.
code
C45327
Contributing_Source
- GDC
- NICHD
ICD-O-3_Code
9725/3
in_subset
- GDC Value Terminology
- NICHD Terminology
- Mapped ICDO3.2 Morphology Terminology
- Mapped ICDO3.1 Morphology PT Terminology
- Mapped ICDO3.2 Terminology
- Pediatric Hematology-Oncology Terminology
- Mapped ICDO3.1 Terminology
- Mapped ICDO3.1 Morphology Terminology
- GDC Terminology
- NCIt Neoplasm Core Terminology
- Mapped ICDO3.2 Morphology PT Terminology
Is_Value_For_GDC_Property
Legacy Concept Name
Hydroa_Vacciniforme-Like_Cutaneous_T-Cell_Lymphoma
Maps_To
- 9725/3
- Hydroa vacciniforme-like lymphoproliferative disorder
- Hydroa vacciniforme-like lymphoma
Neoplastic_Status
Undetermined
Preferred_Name
Hydroa Vacciniforme Lymphoproliferative Disorder
Semantic_Type
Neoplastic Process
UMLS_CUI
C1708397
class Relations
Equivalent to