OntologiesncitclassesNCIT:C45327   
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Hydroa Vacciniforme Lymphoproliferative Disorder
http://purl.obolibrary.org/obo/NCIT_C45327

A rare, EBV-positive cutaneous T-cell lymphoproliferative disorder, composed of CD8 positive cytotoxic T-lymphocytes. It affects children, almost exclusively in Latin America and Asia. Patients present with papulovesicular skin lesions, clinically resembling hydroa vacciniforme, in areas of sun-exposed skin.

Exact Synonyms
HV LPD
HV-Like LPD
HV-Like Lymphoma
HV-LPD
Hydroa Vacciniforme Lymphoproliferative Disorder
Hydroa Vacciniforme-Like Cutaneous T-Cell Lymphoma
Hydroa vacciniforme-like lymphoma
Hydroa Vacciniforme-Like Lymphoma
Hydroa Vacciniforme-Like Lymphoproliferative Disorder
class Information
ALT_DEFINITION

In contrast to hydroa vacciniforme (HV), HV-like lymphoma is not induced by sun exposure and the lesions can occur in both sun-exposed and covered body areas. It affects children, almost exclusively in Latin America and Asia.

code

C45327

Contributing_Source
  • GDC
  • NICHD
ICD-O-3_Code

9725/3

Legacy Concept Name

Hydroa_Vacciniforme-Like_Cutaneous_T-Cell_Lymphoma

Maps_To
  • 9725/3
  • Hydroa vacciniforme-like lymphoproliferative disorder
  • Hydroa vacciniforme-like lymphoma
Neoplastic_Status

Undetermined

Preferred_Name

Hydroa Vacciniforme Lymphoproliferative Disorder

Semantic_Type

Neoplastic Process

UMLS_CUI

C1708397

class Relations