Primary Mediastinal Large B-Cell Lymphoma
A large B-cell non-Hodgkin lymphoma arising in the mediastinum. Morphologically it is characterized by a massive diffuse lymphocytic proliferation associated with compartmentalizing fibrosis. Response to intensive chemotherapy, with or without radiotherapy, is usually good. (WHO, 2001)
Exact Synonyms
B-Cell Diffuse Large Cell Lymphoma of Mediastinum
B-Cell Diffuse Large Cell Lymphoma of the Mediastinum
Mediastinal (thymic) large B-cell lymphoma, unspecified site
Mediastinal (thymic) large B-cell lymphoma
Mediastinal (Thymic) Large B-Cell Lymphoma
Mediastinal B-Cell Diffuse Large Cell Lymphoma
Mediastinal Diffuse Large Cell Lymphoma with Sclerosis
Mediastinal large B-cell lymphoma
PMBL
PMLCL
Primary Mediastinal (Thymic) Large B-Cell Lymphoma
Primary Mediastinal Clear Cell Lymphoma of B-Cell Type
Primary Mediastinal Large B-Cell Lymphoma
Thymic large B-cell lymphoma
class Information
code
C9280
Contributing_Source
- Cellosaurus
- CPTAC
- CTEP
- CTRP
- GDC
- mCode
Display_Name
Primary Mediastinal (Thymic) Large B-Cell Lymphoma
ICD-O-3_Code
9679/3
in_subset
- GDC Terminology
- mCode Primary Malignant Neoplasm Disorder Value Set
- NCI CTEP SDC Non-Hodgkin Lymphoma Sub-Category Terminology
- mCode Primary Cancer Disorder Value Set
- CTRP Disease Terminology
- mCode Elixhauser Lymphoma Value Set
- Mapped ICDO3.1 Morphology PT Terminology
- NCI CTEP Simplified Disease Classification Terminology
- mCode Cancer Disorder Value Set
- Mapped ICDO3.2 Terminology
- CPTAC Neoplasms Codelist
- Cellosaurus Disease Terminology
- Mapped ICDO3.2 Morphology PT Terminology
- Cellosaurus Terminology
- NCIt Neoplasm Core Terminology
- Mapped ICDO3.1 Terminology
- CTRP Terminology
- GDC Value Terminology
- Mapped ICDO3.2 Morphology Terminology
- Mapped ICDO3.1 Morphology Terminology
- CPTAC Codelists Terminology
- CPTAC Terminology
- oncotree_slim
- mCode Terminology
Is_Value_For_GDC_Property
Legacy Concept Name
Mediastinal_Thymic_Large_B-Cell_Cell_Lymphoma
Maps_To
- 9679/3
- Mediastinal (thymic) large B-cell lymphoma, intrathoracic lymph nodes
- Mediastinal large B-cell lymphoma
- Mediastinal (thymic) large B-cell lymphoma
- Thymic large B-cell lymphoma
Neoplastic_Status
Malignant
Preferred_Name
Primary Mediastinal Large B-Cell Lymphoma
Semantic_Type
Neoplastic Process
UMLS_CUI
C1292754
class Relations
Equivalent to
- (Mediastinal Non-Hodgkin LymphomaandThymic LymphomaandDiffuse Large B-Cell LymphomaandDisease_Has_Normal_Cell_OriginsomeThymic B-LymphocyteandDisease_Has_Abnormal_CellsomeNeoplastic Large B-Lymphocyte with Pale CytoplasmandDisease_Has_FindingsomeFibrosisandDisease_Has_FindingsomeIncreased NFkappaB Pathway ActivationandDisease_May_Have_Cytogenetic_AbnormalitysomeGain of Chromosome 9pandDisease_May_Have_FindingsomeRapidly Enlarging MassandDisease_May_Have_FindingsomeLocalized DiseaseandDisease_May_Have_FindingsomeCD30-Positive Neoplastic Cells PresentandDisease_May_Have_Associated_DiseasesomeSuperior Vena Cava SyndromeandDisease_Excludes_Molecular_AbnormalitysomeClonal BCL2 Gene RearrangementandDisease_Mapped_To_ChromosomesomeHuman Chromosome 9andDisease_May_Have_Molecular_AbnormalitysomePDCD1LG2 Gene Overexpression)