Articles - 1x80 mentioned but not cited (1)
- Nuclear inelastic scattering and Mössbauer spectroscopy as local probes for ligand binding modes and electronic properties in proteins: vibrational behavior of a ferriheme center inside a β-barrel protein. Moeser B, Janoschka A, Wolny JA, Paulsen H, Filippov I, Berry RE, Zhang H, Chumakov AI, Walker FA, Schünemann V. J Am Chem Soc 134 4216-4228 (2012)
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- Mitochondrial modulation: reversible phosphorylation takes center stage? Pagliarini DJ, Dixon JE. Trends Biochem Sci 31 26-34 (2006)
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- Profiling phosphoproteins of yeast mitochondria reveals a role of phosphorylation in assembly of the ATP synthase. Reinders J, Wagner K, Zahedi RP, Stojanovski D, Eyrich B, van der Laan M, Rehling P, Sickmann A, Pfanner N, Meisinger C. Mol Cell Proteomics 6 1896-1906 (2007)
- BCKDH: the missing link in apicomplexan mitochondrial metabolism is required for full virulence of Toxoplasma gondii and Plasmodium berghei. Oppenheim RD, Creek DJ, Macrae JI, Modrzynska KK, Pino P, Limenitakis J, Polonais V, Seeber F, Barrett MP, Billker O, McConville MJ, Soldati-Favre D. PLoS Pathog 10 e1004263 (2014)
- Structural basis for inactivation of the human pyruvate dehydrogenase complex by phosphorylation: role of disordered phosphorylation loops. Kato M, Wynn RM, Chuang JL, Tso SC, Machius M, Li J, Chuang DT. Structure 16 1849-1859 (2008)
- A novel branched-chain amino acid metabolon. Protein-protein interactions in a supramolecular complex. Islam MM, Wallin R, Wynn RM, Conway M, Fujii H, Mobley JA, Chuang DT, Hutson SM. J Biol Chem 282 11893-11903 (2007)
- Branched-chain amino acid metabolon: interaction of glutamate dehydrogenase with the mitochondrial branched-chain aminotransferase (BCATm). Islam MM, Nautiyal M, Wynn RM, Mobley JA, Chuang DT, Hutson SM. J Biol Chem 285 265-276 (2010)
- Phenylbutyrate therapy for maple syrup urine disease. Brunetti-Pierri N, Lanpher B, Erez A, Ananieva EA, Islam M, Marini JC, Sun Q, Yu C, Hegde M, Li J, Wynn RM, Chuang DT, Hutson S, Lee B. Hum Mol Genet 20 631-640 (2011)
- Benzothiophene carboxylate derivatives as novel allosteric inhibitors of branched-chain α-ketoacid dehydrogenase kinase. Tso SC, Gui WJ, Wu CY, Chuang JL, Qi X, Skvora KJ, Dork K, Wallace AL, Morlock LK, Lee BH, Hutson SM, Strom SC, Williams NS, Tambar UK, Wynn RM, Chuang DT. J Biol Chem 289 20583-20593 (2014)
- Two novel mutations in the BCKDK (branched-chain keto-acid dehydrogenase kinase) gene are responsible for a neurobehavioral deficit in two pediatric unrelated patients. García-Cazorla A, Oyarzabal A, Fort J, Robles C, Castejón E, Ruiz-Sala P, Bodoy S, Merinero B, Lopez-Sala A, Dopazo J, Nunes V, Ugarte M, Artuch R, Palacín M, Rodríguez-Pombo P, Alcaide P, Navarrete R, Sanz P, Font-Llitjós M, Vilaseca MA, Ormaizabal A, Pristoupilova A, Agulló SB. Hum Mutat 35 470-477 (2014)
- Structure-based design and mechanisms of allosteric inhibitors for mitochondrial branched-chain α-ketoacid dehydrogenase kinase. Tso SC, Qi X, Gui WJ, Chuang JL, Morlock LK, Wallace AL, Ahmed K, Laxman S, Campeau PM, Lee BH, Hutson SM, Tu BP, Williams NS, Tambar UK, Wynn RM, Chuang DT. Proc Natl Acad Sci U S A 110 9728-9733 (2013)
- A versatile conformational switch regulates reactivity in human branched-chain alpha-ketoacid dehydrogenase. Machius M, Wynn RM, Chuang JL, Li J, Kluger R, Yu D, Tomchick DR, Brautigam CA, Chuang DT. Structure 14 287-298 (2006)
- Phosphorylation regulates assembly of the caspase-6 substrate-binding groove. Velázquez-Delgado EM, Hardy JA. Structure 20 742-751 (2012)
- Characterization of testis-specific isoenzyme of human pyruvate dehydrogenase. Korotchkina LG, Sidhu S, Patel MS. J Biol Chem 281 9688-9696 (2006)
- Determination of pre-steady-state rate constants on the Escherichia coli pyruvate dehydrogenase complex reveals that loop movement controls the rate-limiting step. Balakrishnan A, Nemeria NS, Chakraborty S, Kakalis L, Jordan F. J Am Chem Soc 134 18644-18655 (2012)
- Dual specificity phosphatases 18 and 21 target to opposing sides of the mitochondrial inner membrane. Rardin MJ, Wiley SE, Murphy AN, Pagliarini DJ, Dixon JE. J Biol Chem 283 15440-15450 (2008)
- Molecular and structural analyses of maple syrup urine disease and identification of a founder mutation in a Portuguese Gypsy community. Quental S, Macedo-Ribeiro S, Matos R, Vilarinho L, Martins E, Teles EL, Rodrigues E, Diogo L, Garcia P, Eusébio F, Gaspar A, Sequeira S, Furtado F, Lança I, Amorim A, Prata MJ. Mol Genet Metab 94 148-156 (2008)
- Structural and biochemical characterization of human mitochondrial branched-chain α-ketoacid dehydrogenase phosphatase. Wynn RM, Li J, Brautigam CA, Chuang JL, Chuang DT. J Biol Chem 287 9178-9192 (2012)
- Analysis of gene mutations in Chinese patients with maple syrup urine disease. Yang N, Han L, Gu X, Ye J, Qiu W, Zhang H, Gong Z, Zhang Y. Mol Genet Metab 106 412-418 (2012)
- Inferring high-confidence human protein-protein interactions. Yu X, Wallqvist A, Reifman J. BMC Bioinformatics 13 79 (2012)
- CLC anion channel regulatory phosphorylation and conserved signal transduction domains. Miyazaki H, Yamada T, Parton A, Morrison R, Kim S, Beth AH, Strange K. Biophys J 103 1706-1718 (2012)
- Conformational ensemble modulates cooperativity in the rate-determining catalytic step in the E1 component of the Escherichia coli pyruvate dehydrogenase multienzyme complex. Kale S, Jordan F. J Biol Chem 284 33122-33129 (2009)
- Dendritic Cells Require PINK1-Mediated Phosphorylation of BCKDE1α to Promote Fatty Acid Oxidation for Immune Function. Basit F, de Vries IJM. Front Immunol 10 2386 (2019)
- Molecular characterization of maple syrup urine disease patients from Tunisia. Jaafar N, Moleirinho A, Kerkeni E, Monastiri K, Seboui H, Amorim A, Prata MJ, Quental S. Gene 517 116-119 (2013)
- Synthesis and conformational analysis of stevastelin C3 analogues and their activity against the dual-specific vaccina H1-related phosphatase. Bisek N, Wetzel S, Arndt HD, Waldmann H. Chemistry 14 8847-8860 (2008)
- Fourteen new mutations of BCKDHA, BCKDHB and DBT genes associated with maple syrup urine disease (MSUD) in Malaysian population. Ali EZ, Ngu LH. Mol Genet Metab Rep 17 22-30 (2018)
- Case Reports Silico analysis of a novel mutation c.550delT in a Chinese patient with maple syrup urine disease. Li W, Meng X, Wang W, Lv J, Sun Y, Lv Y, Wang C, Wang H, Wang M, Song D. Clin Case Rep 6 1989-1993 (2018)
- Whole-body metabolic fate of branched-chain amino acids. Blair MC, Neinast MD, Arany Z. Biochem J 478 765-776 (2021)
- A Metabolomics-Based Investigation of the Effects of a Short-Term Body Weight Reduction Program in a Cohort of Adolescents with Obesity: A Prospective Interventional Clinical Study. Rigamonti AE, Frigerio G, Caroli D, De Col A, Cella SG, Sartorio A, Fustinoni S. Nutrients 15 529 (2023)
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