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Ontologies▸ordo▸classes▸ORDO:704   
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Pemphigus vulgaris
http://www.orpha.net/ORDO/Orphanet_704

A rare autoimmune bullous skin diseases characterized by painful, flaccid blisters and erosions of the oral mucosa, predominantly involving the buccal area, and with or without extension to the epidermis. Mucosa of the larynx, oesophagus, conjunctiva, nose, genitalia and anus, are less frequently affected.

    class Information
    definition_citation

    Orphanet

    has_age_of_onset
    • Adult
    • Childhood
    • Elderly
    has_dbxref
    has_inheritance

    Not applicable

    notation

    ORPHA:704

    present_in
    • Bulgaria AND has_annual_incidence_average_value : 0.47 AND has_annual_incidence_range : 1-9 / 1 000 000
    • Europe AND has_point_prevalence_average_value : 18.0 AND has_point_prevalence_range : 1-5 / 10 000
    • Finland AND has_annual_incidence_average_value : 0.076 AND has_annual_incidence_range : <1 / 1 000 000
    • France AND has_annual_incidence_average_value : 0.13 AND has_annual_incidence_range : 1-9 / 1 000 000
    • Germany AND has_point_prevalence_average_value : 9.482 AND has_point_prevalence_range : 1-9 / 100 000
    • Tunisia AND has_annual_incidence_average_value : 0.25 AND has_annual_incidence_range : 1-9 / 1 000 000
    • United Kingdom AND has_annual_incidence_average_value : 0.7 AND has_annual_incidence_range : 1-9 / 1 000 000
    • United States AND has_annual_incidence_average_value : 0.42 AND has_annual_incidence_range : 1-9 / 1 000 000
    class Relations